Spontaneous arterial perforation: The Ehlers-Danlos specter
نویسندگان
چکیده
منابع مشابه
[Ehlers-Danlos syndrome].
We have described a patient with type 4 Ehlers-Danlos syndrome who died of a ruptured pulmonary artery. Of the six subtypes of Ehlers-Danlos syndrome, which can usually be clinically differentiated, only types 1 and 4 appear to be associated with a substantial risk of arterial rupture.
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448 BMJ | 1 SEPTEMBER 2007 | VoluME 335 hinder implementation of these recommendations. Recognising the condition and the impact it can have on the lives of patients and their families is therefore a necessary preliminary to improving care. • People with severe CFS/ME who are housebound or need prolonged bed rest require specialised care, but evidence is lacking about which treatments are most ...
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ژورنال
عنوان ژورنال: Journal of Vascular Surgery
سال: 1987
ISSN: 0741-5214
DOI: 10.1016/0741-5214(87)90133-9